European Journal of Vascular & Endovascular Surgery
Volume 35, Issue 2 , Pages 181-186 , February 2008

Thoracoabdominal Aortic Aneurysm Repair in Patients with Marfan Syndrome

  • G. Mommertz

      Affiliations

    • European Vascular Center Aachen-Maastricht, Department of Vascular Surgery, University Hospital Aachen and Maastricht, Germany
  • ,
  • F. Sigala

      Affiliations

    • European Vascular Center Aachen-Maastricht, Department of Vascular Surgery, University Hospital Aachen and Maastricht, Germany
  • ,
  • S. Langer

      Affiliations

    • European Vascular Center Aachen-Maastricht, Department of Vascular Surgery, University Hospital Aachen and Maastricht, Germany
  • ,
  • T.A. Koeppel

      Affiliations

    • European Vascular Center Aachen-Maastricht, Department of Vascular Surgery, University Hospital Aachen and Maastricht, Germany
  • ,
  • W.H. Mess

      Affiliations

    • European Vascular Center Aachen-Maastricht, Department of Neurophysiology, University Hospital Maastricht, The Netherlands
  • ,
  • G.W.H. Schurink

      Affiliations

    • European Vascular Center Aachen-Maastricht, Department of Vascular Surgery, University Hospital Maastricht, The Netherlands
  • ,
  • M.J. Jacobs

      Affiliations

    • European Vascular Center Aachen-Maastricht, Department of Vascular Surgery, University Hospital Aachen and Maastricht, Germany
    • European Vascular Center Aachen-Maastricht, Department of Vascular Surgery, University Hospital Maastricht, The Netherlands
    • Corresponding Author InformationCorresponding author. M. J. Jacobs, MD, Department of Vascular Surgery, University Hospital Maastricht, P.O. Box 5800, 6202 AZ Maastricht, The Netherlands.

,Accepted 16 October 2007.

References 

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  2. Gray JR, Bridges AB, Faed MJ, Pringle T, Baines P, Dean J, et al. Ascertainment and severity of Marfan syndrome in a Scottish population. J Med Genet. 1994;31:51–54
  3. Ramirez F, Dietz HC. Therapy insight: aortic aneurysm and dissection in Marfan's syndrome. Nat Clin Pract Cardiovasc Med. 2004;1:31–36
  4. Murdoch JL, Walker BA, Halpern BL, Kuzma JW, Mc Kusick VA. Life expectancy and causes of death in the Marfan syndrome. N Engl J Med. 1972;286:804–808
  5. Finkbohner R, Johnston D, Crawford ES, Coselli J, Milewicz DM. Marfan syndrome. Long-term survival and complications after aortic aneurysm repair. Circulation. 1995;91:728–733
  6. Roseborough GS, Williams GM. Marfan and other connective tissue disorders: conservative and surgical considerations. Semin Vasc Surg. 2000;13:272–282
  7. Silverman DI, Burton KJ, Gray J, Bosner MS, Kouchoukos NT, Roman MJ, et al. Life expectancy in the Marfan syndrome. Am J Cardiol. 1995;75:157–160
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  9. Milewicz DM, Dietz HC, Miller DC. Treatment of aortic disease in patients with Marfan syndrome. Circulation. 2005;111:e150–e157
  10. Coselli JS, Le Maire SA, Conklin LD, Koksoy C, Schmittling ZC. Morbidity and mortality after extent II thoracoabdominal aortic aneurysm repair. Ann Thorac Surg. 2002;73:1107–1115
  11. Jacobs MJ, de Mol BA, Elenbaas T, Mess WH, Kalkman CJ, Schurink GW, et al. Spinal cord blood supply in patients with thoracoabdominal aortic aneurysms. J Vasc Surg. 2002;35:30–37
  12. Jacobs MJ, Mess WH. The role of evoked potential monitoring in operative management of type I and type II thoracoabdominal aortic aneurysms. Semin Thorac Cardiovasc Surg. 2003;15:353–364
  13. Jacobs MJ, Mess W, Mochtar B, Nijenhuis RJ, Statius van Eps RG, Schurink GW. The value of motor evoked potentials in reducing paraplegia during thoracoabdominal aneurysm repair. J Vasc Surg. 2006;43:239–246
  14. Dardik A, Perler BA, Roseborough GS, Williams GM. Aneurysmal expansion of the visceral patch after thoracoabdominal aortic replacement: an argument for limiting patch size?. J Vasc Surg. 2001;34:405–409
  15. Coselli JS, Bozinovski J, Le Maire SA. Open surgical repair of 2286 thoracoabdominal aortic aneurysms. Ann Thorac Surg. 2007;83:S862–S864
  16. Mac Arthur RG, Carter SA, Coselli JS, Le Maire SA. Organ protection during thoracoabdominal aortic surgery: rationale for a multimodality approach. Semin Cardiothorac Vasc Anesth. 2005;9:143–149
  17. Le Maire SA, Carter SA, Volguina IV, Laux AT, Milewicz DM, Borsato GW, et al. Spectrum of aortic operations in 300 patients with confirmed or suspected Marfan syndrome. Ann Thorac Surg. 2006;81:2063–2078
  18. Kalkat MS, Rahman I, Kotidis K, Davies B, Bonser RS. Presentation and outcome of Marfan´s syndrome patients with dissection and thoraco-abdominal aortic aneurysm. Eur J Cardiothorac Surg. 2007;32:250–254
  19. Albornoz G, Coady MA, Roberts M, Davies RR, Tranquilli M, Ritto JA, et al. Familial thoracic aortic aneurysms and dissections–incidence, modes of inheritance, and phenotypic patterns. Ann Thorac Surg. 2006;82:1400–1405
  20. Ince H, Rehders TC, Petsch M, Kische S, Nienaber CA. Stent-grafts in patients with Marfan syndrome. J Endovasc Ther. 2005;12:82–88

 Presented at the XXI Annual meeting of the ESVS, Madrid, Spain, September 20–23, 2007.

PII: S1078-5884(07)00672-7

doi: 10.1016/j.ejvs.2007.10.013

European Journal of Vascular & Endovascular Surgery
Volume 35, Issue 2 , Pages 181-186 , February 2008